Malignant Peripheral Nerve Sheath Tumor Staging on PET-CT Imaging in a Patient with Neurofibromatosis Type I
نویسنده
چکیده
Submit Manuscript | http://medcraveonline.com Malignant peripheral nerve sheath tumor (MPNST) is a rare tumor group seen in neurofibromatosis type I patients. There are few reports on PET-CT imaging of this rare entity in literature. FDG PET-CT is a part of the conventional work-up among a variety of cancer patients. Nevertheless, in certain clinical situations PETCT may be of great significance, especially as treatment algorithm or differential diagnosis of benign and malign tumors. In this rare case, we aimed to emphasize the importance of PET-CT imaging in demonstrating the prevalence of a 24-year-old male patient with neurofibromatosis type 1.
منابع مشابه
Multimodal Imaging in Neurofibromatosis Type 1-associated Nerve Sheath Tumors.
UNLABELLED Neurofibromatosis type 1 (NF1) is a neurogenetic disorder. Individuals with NF1 may develop a variety of benign and malignant tumors of which peripheral nerve sheath tumors represent the most frequent entity. Plexiform neurofibromas may demonstrate a locally destructive growth pattern, may cause severe symptoms and may undergo malignant transformation into malignant peripheral nerve ...
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Malignant peripheral nerve sheath tumor (MPNST) is a rare nerve sheath tumor derived from Schwann cells or pleuripotent cells of neural crest. Neurogenic tumors make about 10-20% of all mediastinal tumors. Incidence of MPNST is 0.001% in general population and 0.16% in patients with neurofibromatosis I (NF I). We report a case of 60 year female presenting with progressive cough and breathlessne...
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